Pediatric Factor VII Deficiency Questions & Answers

Updated: Jun 22, 2021
  • Author: Helge Dirk Hartung, MD; Chief Editor: Hassan M Yaish, MD  more...
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Questions & Answers

Overview

What is pediatric factor VII deficiency?

What is the pathophysiology of pediatric factor VII deficiency?

How is pediatric factor VII deficiency classified?

What is the prevalence of pediatric factor VII deficiency in the US?

What is the global prevalence of pediatric factor VII deficiency?

What is the cause of mortality from pediatric factor VII deficiency?

What are the sexual predilections of pediatric factor VII deficiency?

At what age does pediatric factor VII deficiency typically present?

Presentation

Which clinical history findings are characteristic of pediatric factor VII deficiency?

Which physical findings are characteristic of pediatric factor VII deficiency?

DDX

Which conditions are included in the differential diagnoses of pediatric factor VII deficiency?

Workup

What is the role of lab testing in the workup of pediatric factor VII deficiency?

What is the role of imaging studies in the workup of pediatric factor VII deficiency?

Treatment

How is acute bleeding treated in patients with pediatric factor VII deficiency?

When is prophylaxis indicated in the treatment of pediatric factor VII deficiency?

What is the role of surgery in the treatment of pediatric factor VII deficiency?

Which specialist consultations are beneficial to patients with pediatric factor VII deficiency?

Which activity modifications are used in the treatment of pediatric factor VII deficiency?

Follow-up

How should pediatric factor VII deficiency be monitored?

How are acute bleeds prevented in pediatric factor VII deficiency?

What are the possible complications of pediatric factor VII deficiency?

What is included in patient education about pediatric factor VII deficiency?