Supravalvular Ring Mitral Stenosis Differential Diagnoses

Updated: Dec 15, 2020
  • Author: Michael D Pettersen, MD; Chief Editor: Howard S Weber, MD, FSCAI  more...
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Diagnostic Considerations

Important considerations

It is important that clinicians recognize supravalvar mitral ring as an associated defect in patients with coarctation or subaortic stenosis.

Clinicians should also recognize associated abnormalities of the mitral valve and left ventricular (LV) outflow tract in patients with supravalvar mitral ring.

Do not fail to identify the presence of a supravalvar mitral ring in patients with symptoms and signs of mitral stenosis.

Special concerns

Supravalvar mitral ring may not be easily detectable in children with congenital heart disease (CHD). Therefore, awareness of the problem and careful echocardiographic screening are important in all children with CHD.

Differential Diagnoses