Retroperitoneal Fibrosis Questions & Answers

Updated: Sep 02, 2021
  • Author: Chandra Shekhar Biyani, MS, MBBS, DUrol, FRCS(Urol), FEBU; Chief Editor: Bradley Fields Schwartz, DO, FACS  more...
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Questions & Answers

Overview

What is the clinical presentation of retroperitoneal fibrosis (RPF)?

What are the signs and symptoms of retroperitoneal fibrosis (RPF)?

What is required to diagnosis retroperitoneal fibrosis (RPF)?

Which physical exam findings suggest retroperitoneal fibrosis (RPF)?

Which physical findings may be due to late complications of retroperitoneal fibrosis (RPF)?

What is the role of lab testing in the workup of retroperitoneal fibrosis (RPF)?

Which imaging studies are performed in the workup of retroperitoneal fibrosis (RPF)?

What is the role of biopsy in the workup of retroperitoneal fibrosis (RPF)?

What is included in optimal care of retroperitoneal fibrosis (RPF)?

Which surgical interventions are used in the treatment of retroperitoneal fibrosis (RPF)?

Which medications are used in the treatment of retroperitoneal fibrosis (RPF)?

What is retroperitoneal fibrosis (RPF)?

What is the anatomy of the retroperitoneum relevant to retroperitoneal fibrosis (RPF)?

What is the pathogenesis of retroperitoneal fibrosis (RPF)?

What are the pathogenic features of idiopathic retroperitoneal fibrosis (RPF)?

What is the prevalence of retroperitoneal fibrosis (RPF)?

What is the mortality and morbidity associated with retroperitoneal fibrosis (RPF)?

Which patient groups have the highest prevalence of retroperitoneal fibrosis (RPF)?

Presentation

Which clinical history findings are characteristic of retroperitoneal fibrosis (RPF)?

DDX

Which conditions should be included in the differential diagnoses of retroperitoneal fibrosis (RPF)?

Workup

Which lab tests are performed in the workup of retroperitoneal fibrosis (RPF)?

What is the role of imaging studies in the workup of retroperitoneal fibrosis (RPF)?

What is the role of plain radiography in the workup of retroperitoneal fibrosis (RPF)?

What is the role of IV urography in the workup of retroperitoneal fibrosis (RPF)?

What is the role of retrograde pyelography in the workup of retroperitoneal fibrosis (RPF)?

What is the role of lymphangiography in the workup of retroperitoneal fibrosis (RPF)?

What is the role of ultrasonography in the workup of retroperitoneal fibrosis (RPF)?

What is the role of CT scanning in the workup of retroperitoneal fibrosis (RPF)?

What is the role of MRI in the workup of retroperitoneal fibrosis (RPF)?

What is the role of PET scanning in the workup of retroperitoneal fibrosis (RPF)?

Which histologic findings are characteristic of retroperitoneal fibrosis (RPF)?

How is a diagnosis of retroperitoneal fibrosis (RPF) confirmed?

Treatment

How is retroperitoneal fibrosis (RPF) treated?

What is the role of corticosteroids in the treatment of retroperitoneal fibrosis (RPF)?

What are the adverse effects of long-term corticosteroid treatment for retroperitoneal fibrosis (RPF)?

What is the role of tamoxifen in the treatment of retroperitoneal fibrosis (RPF)?

What is the role of mycophenolate mofetil in the treatment of retroperitoneal fibrosis (RPF)?

What is the role of azathioprine in the treatment of retroperitoneal fibrosis (RPF)?

What is the role of rituximab in the treatment of retroperitoneal fibrosis (RPF)?

What is the role of medroxyprogesterone acetate in the treatment of retroperitoneal fibrosis (RPF)?

What is the role of surgery in the treatment of retroperitoneal fibrosis (RPF)?

Which specialist consultations are beneficial to patients with retroperitoneal fibrosis (RPF)?

Medications

What is the goal of medical treatment of retroperitoneal fibrosis (RPF)?

Which medications in the drug class Estrogen receptor antagonists are used in the treatment of Retroperitoneal Fibrosis?

Which medications in the drug class Immunosuppressives are used in the treatment of Retroperitoneal Fibrosis?

Which medications in the drug class Glucocorticoids are used in the treatment of Retroperitoneal Fibrosis?

Follow-up

What is included in the long-term monitoring of patients with retroperitoneal fibrosis (RPF)?

What is included in inpatient care for retroperitoneal fibrosis (RPF)?

What are the possible complications of retroperitoneal fibrosis (RPF)?

What is the prognosis of retroperitoneal fibrosis (RPF)?

What is included in patient education about retroperitoneal fibrosis (RPF)?