Naegeli-Franceschetti-Jadassohn Syndrome Treatment & Management

Updated: Aug 30, 2018
  • Author: Rebekah H Clifford, MD; Chief Editor: Dirk M Elston, MD  more...
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Treatment

Medical Care

No treatment is effective for Naegeli-Franceschetti-Jadassohn (NFJ) syndrome. As with other ectodermal dysplasias, exposure to heat should be limited and sufficient hydration is recommended. Tooth care to prevent early caries is indicated. Doxycycline has been found to interfere with tumor necrosis factor-alpha (TNF-alpha)–mediated signaling and apoptosis in vitro and may have a role in future treatment. [2]

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Activity

Sports-related exercise should be restricted to only nonexhausting activities. In particular, patients with Naegeli-Franceschetti-Jadassohn (NFJ) syndrome can be allowed to swim.

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