Proliferating Pilar Tumor Treatment & Management

Updated: Jan 27, 2020
  • Author: Marjon Vatanchi, MD; Chief Editor: William D James, MD  more...
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Approach Considerations

Complete excision with a margin of normal tissue is recommended. No consensus has been reached regarding the margin size of normal tissue.

In a case study of malignant proliferating pilar tumor (PPT) with multinodal metastasis, wide local excision with 1-cm margins was performed, followed by adjuvant chemotherapy and radiation to prevent recurrence. [28]

Of note, in 2017 a case report described successful treatment of a malignant proliferating trichilemmal tumor with radical radiotherapy in a patient who was not a good candidate for surgery (aged 93 years, with multiple comorbidities). [29]


Long-Term Monitoring

Monitor the patient for local recurrence and periodically examine the lymph nodes to rule out metastasis. No recommendations exist for the interval or length of follow-up.

Screening for proliferating pilar tumor (PPT) is suggested in patients with keratitis-ichthyosis-deafness (KID) syndrome. [30]