Primary Ciliary Dyskinesia Follow-up

Updated: Oct 17, 2017
  • Author: Girish D Sharma, MD, FCCP, FAAP; Chief Editor: Denise Serebrisky, MD  more...
  • Print
Follow-up

Deterrence/Prevention

Recommendations from the European Respiratory Society task force on diagnostic and treatment approaches in children with PCD include exclusion of this diagnosis in children found to have situs inversus totalis or any heterotaxic syndrome, in the siblings of probands, in babies with otherwise unexplained neonatal respiratory distress other features of PCD are present, in children with chronic productive cough, and in patients with bronchiectasis of unknown cause, particularly if other features of PCD are present. [32]

Next:

Prognosis

See the list below:

  • The progression of lung disease varies and is affected by the time of diagnosis, the ability of medical treatment to control symptoms, and the prevention of complications that affect the quality of life.

  • Some individuals have a normal or near normal lifespan. No studies have examined the impact of current symptomatic therapies on the course of disease.

Previous
Next:

Patient Education

See the list below:

  • Genetic counseling should be offered to parents of newly diagnosed infants and children. The importance of regular health monitoring should be emphasized. Counsel patients to avoid smoke, allergens, environmental irritants, and exposure to respiratory pathogens.

  • For patient education resources, see the Procedures Center, as well as Bronchoscopy.

Previous